Causes

Pulmonary Fibrosis

There are many causes of Pulmonary Fibrosis (PF). Your doctor will perform tests to confirm that you have PF and to look for a cause. 

Pulmonary Fibrosis with a known cause may be secondary to: 

  • Autoimmune disease (e.g. Rheumatoid arthritis, scleroderma)  
  • Non-organic exposures (e.g. asbestos, silica, certain medications) 
  • Organic exposures (e.g. hypersensitivity pneumonitis from mould or birds) 
  • Smoking (e.g. pulmonary Langerhans cell histiocytosis) 

 “Idiopathic” diseases refer to specific diseases where the underlying cause is unknown. The most common condition in this group of diseases is Idiopathic Pulmonary Fibrosis (IPF). Other conditions include Idiopathic Non-Specific Interstitial Pneumonia (NSIP) and Cryptogenic Organising Pneumonia (COP).