Scleroderma and interstitial lung disease

In this webinar from Lung Foundation Australia, Dr Alan Teoh (Respiratory Specialist) and Dr Matthew Parker (Rheumatologist) provide an overview of Scleroderma and an insight into how to navigate the diagnosis and management of your condition.

We were also joined by patient representative, Rossana Reyes, who shared her lived experience and empowering insights into navigating her Scleroderma journey.

Scleroderma, also known as systemic sclerosis, is an autoimmune disease characterised by the thickening and tightening of the skin and narrowing of blood vessels. When it affects the lungs, it is referred to as Systemic Sclerosis-related ILD (SSc-ILD).

The exact cause of scleroderma is unknown, but it is believed to involve genetic predisposition and environmental triggers, such as exposure to crystalline silica in certain industries.

Symptoms vary depending on the organs involved. Common signs include skin changes, Raynaud’s phenomenon, puffy fingers, breathlessness, cough, fatigue, reflux, heart problems, and joint stiffness.

Diagnosis involves a combination of physical examinations, blood tests for antibodies, and various imaging and lung function tests. High-resolution CT scans and lung function tests are crucial for diagnosing SSc-ILD.

Treatment aims to stabilise lung function and prevent further deterioration. Options include immunosuppressive medications, monoclonal antibodies, anti-fibrotic therapies, and in severe cases, stem-cell or lung transplantation. Regular monitoring by a respiratory specialist is essential.

Patients are encouraged to participate in pulmonary rehabilitation, maintain a healthy diet and exercise routine, keep up with vaccinations, and consider oxygen therapy if prescribed. Palliative care may also be beneficial.

Support from a healthcare team, including respiratory specialists, rheumatologists, physiotherapists, dieticians, and counsellors, is vital. If you or someone you know is affected by ILD, reaching out to the Lung Foundation Australia can provide valuable support and information. They are dedicated to helping patients navigate their journey and access the best possible care. For more information and support, individuals can contact the Lung Foundation Australia’s Information and Support Centre at 1800 654 301 or visit their website.