The living with pulmonary arterial hypertension booklet is designed to provide people living with Pulmonary Arterial Hypertension (PAH) an overview of PAH, diagnosis and treatments well as self-management strategies to help you stay well.
PAH is a condition characterised by increased pressure in the lung arteries. The booklet outlines the causes of PAH, including idiopathic origins, genetic factors, and complications from other diseases such as connective tissue disorders, HIV, congenital heart disease, liver disease, and chronic thromboembolic pulmonary hypertension.
Symptoms of PAH can be subtle initially, often noticed during physical activities, and may include shortness of breath, fatigue, dizziness, chest discomfort, irregular heartbeat, and swelling in the legs or abdomen. Diagnosis involves a series of tests, including electrocardiography, echocardiograms, lung function tests, and right heart catheterization, typically conducted at PAH Expert Referral Centres.
Treatment options for PAH focus on medications that open up the blood vessels in the lungs, improve blood flow, and reduce heart strain. These include prostacyclins, endothelin receptor antagonists, PDE-5 inhibitors, and soluble guanylate cyclase stimulators. Supportive medications like diuretics and blood thinners may also be prescribed. Oxygen therapy and participation in clinical trials are additional treatment avenues.
Self-management strategies are emphasised, including maintaining a healthy diet, staying physically active, getting adequate rest, and managing stress. The booklet highlights the importance of regular monitoring and follow-up with healthcare providers to manage symptoms and adjust treatments as needed. Emotional support is crucial, and patients are encouraged to seek help from family, friends, healthcare professionals, and peer support groups.
The booklet also covers practical aspects of living with PAH, such as travel considerations, the importance of vaccinations, and women’s reproductive health, including the risks associated with pregnancy and the need for effective contraception. Overall, the resource aims to empower patients with knowledge and tools to manage their condition and improve their quality of life.
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