Scleroderma and Interstitial Lung Disease Webinar

In this webinar, Dr Alan Teoh (Respiratory Specialist) and Dr Matthew Parker (Rheumatologist) provide an overview of Scleroderma and an insight into how to navigate the diagnosis and management of your condition.

We were also joined by patient representative, Rossana Reyes, who shared her lived experience and empowering insights into navigating her Scleroderma journey.

Scleroderma, also known as systemic sclerosis, is an autoimmune disease characterized by the thickening and tightening of the skin and narrowing of blood vessels. When it affects the lungs, it is referred to as Systemic Sclerosis-related ILD (SSc-ILD).

The exact cause of scleroderma is unknown, but it is believed to involve genetic predisposition and environmental triggers, such as exposure to crystalline silica in certain industries.

Symptoms vary depending on the organs involved. Common signs include skin changes, Raynaud’s phenomenon, puffy fingers, breathlessness, cough, fatigue, reflux, heart problems, and joint stiffness.

Diagnosis involves a combination of physical examinations, blood tests for antibodies, and various imaging and lung function tests. High-resolution CT scans and lung function tests are crucial for diagnosing SSc-ILD.

Systemic sclerosis is a serious condition requiring careful and ongoing management. Most patients can maintain their quality of life and lifespan. Symptoms of systemic sclerosis include Raynaud’s phenomenon, digital ulcers, and joint inflammation. Early intervention and ongoing medical support can significantly improve outcomes for patients.

Treatment aims to stabilise lung function and prevent further deterioration. Treatment options include immunosuppressive medications, monoclonal antibodies, anti-fibrotic therapies, and in severe cases, stem-cell or lung transplantation. Regular monitoring by a respiratory specialist is essential.

Patients are encouraged to participate in pulmonary rehabilitation, maintain a healthy diet and exercise routine, keep up with vaccinations, and consider oxygen therapy if prescribed. Palliative care may also be beneficial.

Support from a healthcare team, including respiratory specialists, rheumatologists, physiotherapists, dieticians, and counsellors, is vital.