Monitoring your pulmonary arterial hypertension

In this video, Dr Claire Ellender (Respiratory & Sleep Physician, Princess Alexandra Hospital) shares her expert knowledge on monitoring your PAH. She provides expert insights into how PAH is monitored and measured, how often you should be monitored, the role of different members of your healthcare team and more.

Pulmonary arterial hypertension (PAH) is a serious condition that requires careful monitoring and management. Doctors assess symptoms like breathlessness, fatigue, and exercise limitations to determine the severity of PAH. They use the New York Heart Association (NYHA) functional class to categorise symptoms from Class I (minimal limitation) to Class IV (severe symptoms).

Initial tests include a six-minute walk test, echocardiogram, and blood tests like BNP to measure heart strain. These tests help classify patients into low, intermediate, or high risk, guiding treatment plans. Follow-up tests every 3-6 months help adjust treatments based on changes in symptoms and test results.

Regular GP visits every 3-6 months are crucial for monitoring liver and kidney function, especially for those on PAH medications. Specialists, such as respiratory physicians or cardiologists, should be seen at least every six months for prescription management.

Exercise is beneficial but should be supervised by healthcare professionals to ensure safety. Pulmonary rehabilitation programs can help improve overall health and manage symptoms.

Mental health is also important. Chronic diseases like PAH can impact psychological well-being. Support from GPs, patient groups, and mental health professionals can be valuable. Mental health care plans can help cover the cost of psychology visits.

Warning signs to watch for include rapidly worsening breathlessness, swelling, chest pain, blackouts, low blood pressure, and heart palpitations. These symptoms should be reported to a healthcare provider immediately.

Expert referral centres for PAH offer comprehensive care with a team of specialists and nurse consultants. Early intervention and regular monitoring can improve treatment effectiveness and patient outcomes.